Intimal pulmonary artery sarcoma presenting as severe dyspnea and right heart insufficiency
Research output: Contribution to journal › Research article › Contributed › peer-review
Contributors
Abstract
BACKGROUND: Pulmonary artery sarcoma is a rare tumor with a poor prognosis.
CASE REPORT: We report the case of a 64-year-old man with an intimal pulmonary artery sarcoma presenting with severe high oxygen flow-demanding dyspnea and weight loss of 12 kg in the last 6 months. On echocardiography, right heart insufficiency, markedly elevated right ventricular pressure, a pressure gradient along the right outflow tract, and a tumor mass adherent to the wall of the truncus pulmonalis were detected. The tentative diagnosis by echocardiographic findings was pulmonary artery sarcoma. Computed tomography of the thorax and 18-fluorodeoxyglucose positron emission tomography showed an advanced local tumor manifestation. Surgical resection of the tumor to improve hemodynamics confirmed the diagnosis.
CONCLUSIONS: Pulmonary artery sarcoma should be considered as a rare differential diagnosis in patients with dyspnea due to right heart failure, particular in the case of additional weight loss, and echocardiographic examination is a useful first diagnostic approach in establishing the diagnosis.
Details
Original language | English |
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Pages (from-to) | 313-316 |
Number of pages | 4 |
Journal | Oncology Research and Treatment |
Volume | 33 |
Issue number | 6 |
Publication status | Published - 2010 |
Peer-reviewed | Yes |
External IDs
Scopus | 77953277881 |
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researchoutputwizard | legacy.publication#36834 |
researchoutputwizard | legacy.publication#36179 |
PubMed | 20523095 |
researchoutputwizard | legacy.publication#36299 |
researchoutputwizard | legacy.publication#41998 |
ORCID | /0000-0001-6022-6827/work/142659540 |
Keywords
Keywords
- Biopsy, Needle, Dyspnea/etiology, Echocardiography, Doppler, Color, Echocardiography, Transesophageal, Fatal Outcome, Heart Failure/etiology, Humans, Lung/pathology, Lymphatic Metastasis/pathology, Male, Middle Aged, Neoplasm Invasiveness, Pneumonectomy, Pulmonary Artery/pathology, Sarcoma/pathology, Thoracoscopy, Tomography, X-Ray Computed, Tunica Intima/pathology, Vascular Neoplasms/pathology