Intimal pulmonary artery sarcoma presenting as severe dyspnea and right heart insufficiency

Publikation: Beitrag in FachzeitschriftForschungsartikelBeigetragenBegutachtung

Beitragende

Abstract

BACKGROUND: Pulmonary artery sarcoma is a rare tumor with a poor prognosis.

CASE REPORT: We report the case of a 64-year-old man with an intimal pulmonary artery sarcoma presenting with severe high oxygen flow-demanding dyspnea and weight loss of 12 kg in the last 6 months. On echocardiography, right heart insufficiency, markedly elevated right ventricular pressure, a pressure gradient along the right outflow tract, and a tumor mass adherent to the wall of the truncus pulmonalis were detected. The tentative diagnosis by echocardiographic findings was pulmonary artery sarcoma. Computed tomography of the thorax and 18-fluorodeoxyglucose positron emission tomography showed an advanced local tumor manifestation. Surgical resection of the tumor to improve hemodynamics confirmed the diagnosis.

CONCLUSIONS: Pulmonary artery sarcoma should be considered as a rare differential diagnosis in patients with dyspnea due to right heart failure, particular in the case of additional weight loss, and echocardiographic examination is a useful first diagnostic approach in establishing the diagnosis.

Details

OriginalspracheEnglisch
Seiten (von - bis)313-316
Seitenumfang4
FachzeitschriftOncology Research and Treatment
Jahrgang33
Ausgabenummer6
PublikationsstatusVeröffentlicht - 2010
Peer-Review-StatusJa

Externe IDs

Scopus 77953277881
researchoutputwizard legacy.publication#36834
researchoutputwizard legacy.publication#36179
PubMed 20523095
researchoutputwizard legacy.publication#36299
researchoutputwizard legacy.publication#41998
ORCID /0000-0001-6022-6827/work/142659540

Schlagworte

Schlagwörter

  • Biopsy, Needle, Dyspnea/etiology, Echocardiography, Doppler, Color, Echocardiography, Transesophageal, Fatal Outcome, Heart Failure/etiology, Humans, Lung/pathology, Lymphatic Metastasis/pathology, Male, Middle Aged, Neoplasm Invasiveness, Pneumonectomy, Pulmonary Artery/pathology, Sarcoma/pathology, Thoracoscopy, Tomography, X-Ray Computed, Tunica Intima/pathology, Vascular Neoplasms/pathology