International consensus statement on the diagnosis and management of phaeochromocytoma and paraganglioma in children and adolescents
Research output: Contribution to journal › Review article › Contributed › peer-review
Contributors
Abstract
Phaeochromocytomas and paragangliomas (PPGL) are rare neuroendocrine tumours that arise not only in adulthood but also in childhood and adolescence. Up to 70-80% of childhood PPGL are hereditary, accounting for a higher incidence of metastatic and/or multifocal PPGL in paediatric patients than in adult patients. Key differences in the tumour biology and management, together with rare disease incidence and therapeutic challenges in paediatric compared with adult patients, mandate close expert cross-disciplinary teamwork. Teams should ideally include adult and paediatric endocrinologists, oncologists, cardiologists, surgeons, geneticists, pathologists, radiologists, clinical psychologists and nuclear medicine physicians. Provision of an international Consensus Statement should improve care and outcomes for children and adolescents with these tumours.
Details
Original language | English |
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Pages (from-to) | 729-748 |
Number of pages | 20 |
Journal | Nature reviews. Endocrinology |
Volume | 20 |
Issue number | 12 |
Publication status | Published - Dec 2024 |
Peer-reviewed | Yes |
External IDs
Scopus | 85201542262 |
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ORCID | /0000-0002-7278-5711/work/173989216 |
Keywords
Keywords
- Humans, Pheochromocytoma/therapy, Paraganglioma/therapy, Adolescent, Child, Adrenal Gland Neoplasms/therapy, Consensus