International consensus statement on the diagnosis and management of phaeochromocytoma and paraganglioma in children and adolescents

Publikation: Beitrag in FachzeitschriftÜbersichtsartikel (Review)BeigetragenBegutachtung

Beitragende

  • Ruth T Casey - , Cambridge University Hospitals NHS Foundation Trust (Autor:in)
  • Emile Hendriks - , Cambridge University Hospitals NHS Foundation Trust (Autor:in)
  • Cheri Deal - , CHU Sainte-Justine (Autor:in)
  • Steven G Waguespack - , University of Texas MD Anderson Cancer Center (Autor:in)
  • Verena Wiegering - , Universitätsklinikum Würzburg (Autor:in)
  • Antje Redlich - , Universitätsklinikum Magdeburg (Autor:in)
  • Scott Akker - , Barts Health NHS Trust (Autor:in)
  • Rathi Prasad - , Queen Mary University of London (Autor:in)
  • Martin Fassnacht - , Universitätsklinikum Würzburg (Autor:in)
  • Roderick Clifton-Bligh - , Royal North Shore Hospital (Autor:in)
  • Laurence Amar - , Assistance publique – Hôpitaux de Paris (Autor:in)
  • Stefan Bornstein - , Medizinische Klinik und Poliklinik III, Universitätsklinikum Carl Gustav Carus Dresden (Autor:in)
  • Letizia Canu - , Azienda Ospedaliera Universitaria (AOU) Careggi (Autor:in)
  • Evangelia Charmandari - , National and Kapodistrian University of Athens, Agia Sofia Children's Hospital, Athens (Autor:in)
  • Alexandra Chrisoulidou - , Theagenio Cancer Hospital (Autor:in)
  • Maria Currás Freixes - , CIBER - Centro de Investigación Biomédica en Red, Instituto de Salud Carlos III (Autor:in)
  • Ronald de Krijger - , Universitätsklinikum Utrecht (Autor:in)
  • Luisa de Sanctis - , University of Turin (Autor:in)
  • Antonio Fojo - , Columbia University Irving Medical Center (CUIMC) (Autor:in)
  • Amol J Ghia - , University of Texas MD Anderson Cancer Center (Autor:in)
  • Angela Huebner - , Klinik und Poliklinik für Kinder- und Jugendmedizin (Autor:in)
  • Vasilis Kosmoliaptsis - , National Institute for Health and Care Research (NIHR), University of Cambridge (Autor:in)
  • Michaela Kuhlen - , Universitätsklinikum Augsburg (Autor:in)
  • Marco Raffaelli - , Catholic University of the Sacred Heart (Autor:in)
  • Charlotte Lussey-Lepoutre - , Hôpital de la Salpêtrière, Sorbonne Université (Autor:in)
  • Stephen D Marks - , Great Ormond Street Hospital for Children NHS Trust, University College London (Autor:in)
  • Naris Nilubol - , National Institutes of Health (NIH) (Autor:in)
  • Mirko Parasiliti-Caprino - , University of Turin (Autor:in)
  • Henri H J L M Timmers - , Radboud University Medical Center (Autor:in)
  • Anna Lena Zietlow - , Professur für Klinische Kinder- und Jugendpsychologie (Autor:in)
  • Mercedes Robledo - , CIBER - Centro de Investigación Biomédica en Red, Instituto de Salud Carlos III (Autor:in)
  • Anne-Paule Gimenez-Roqueplo - , Assistance publique – Hôpitaux de Paris (Autor:in)
  • Ashley B Grossman - , Royal Free London NHS Foundation Trust (Autor:in)
  • David Taïeb - , Assistance publique - Hôpitaux de Marseille (Autor:in)
  • Eamonn R Maher - , NIHR Cambridge Biomedical Research Centre (BCR) (Autor:in)
  • Jacques W M Lenders - , Radboud University Medical Center (Autor:in)
  • Graeme Eisenhofer - , Medizinische Klinik und Poliklinik III, Universitätsklinikum Carl Gustav Carus Dresden (Autor:in)
  • Camilo Jimenez - , University of Texas MD Anderson Cancer Center (Autor:in)
  • Karel Pacak - , Eunice Kennedy Shriver National Institute of Child Health and Human Development (Autor:in)
  • Christina Pamporaki - , Medizinische Klinik und Poliklinik III (Autor:in)

Abstract

Phaeochromocytomas and paragangliomas (PPGL) are rare neuroendocrine tumours that arise not only in adulthood but also in childhood and adolescence. Up to 70-80% of childhood PPGL are hereditary, accounting for a higher incidence of metastatic and/or multifocal PPGL in paediatric patients than in adult patients. Key differences in the tumour biology and management, together with rare disease incidence and therapeutic challenges in paediatric compared with adult patients, mandate close expert cross-disciplinary teamwork. Teams should ideally include adult and paediatric endocrinologists, oncologists, cardiologists, surgeons, geneticists, pathologists, radiologists, clinical psychologists and nuclear medicine physicians. Provision of an international Consensus Statement should improve care and outcomes for children and adolescents with these tumours.

Details

OriginalspracheEnglisch
Seiten (von - bis)729-748
Seitenumfang20
FachzeitschriftNature reviews. Endocrinology
Jahrgang20
Ausgabenummer12
PublikationsstatusVeröffentlicht - Dez. 2024
Peer-Review-StatusJa

Externe IDs

Scopus 85201542262
ORCID /0000-0002-7278-5711/work/173989216

Schlagworte

Schlagwörter

  • Humans, Pheochromocytoma/therapy, Paraganglioma/therapy, Adolescent, Child, Adrenal Gland Neoplasms/therapy, Consensus